Doctors from the Syrian capital, Damascus, announced that they had detected a case of a very rare disease in the world, which was discovered in a Syrian woman in her twenties.
According to the director of Al-Mujtahid Hospital in Damascus, they recorded the fourth case of a rare global disease called ” phagocytic activation syndrome, which is a serious, life-threatening systemic complication.
The disease can occur for many reasons, including inflammatory diseases and autoimmune diseases, and leads to multiple organ failure, according to the director.
The Division of Joint Diseases and Rheumatology received a rare case of a 26-year-old patient who visited the hospital after being diagnosed with (Steel's) disease based on symptoms of a peak fever of 40 degrees Celsius that lasted for more than a week, a non-itchy descriptive skin rash, arthritis that lasted for more than two weeks, and pharyngeal pain with Secondary supporting criteria including lymphadenopathy, elevated hepatic yeast values, and negative ANA and Rf tests.
According to the hospital director, the diagnosis and treatment of the condition occurred within a period of time of approximately 8 months, and that Still's disease is a rare case, but it exists, and its connection to the medication that was taken to treat it showed the condition since taking the first dose, as early diagnosis contributed to saving the patient's life.
It is worth noting that this disease leads to immunodeficiency and the occurrence of severe infections that lead to death, in addition to being a rare disease that results from uncontrolled proliferation and activation of phagocytes that leads to cytokine storms and multiple organ failure.